Hepatic Encephalopathy
Hepatic encephalopathy (also called hepatic coma or portosystemic encephalopathy) is a complex neuropsychiatric syndrome that may complicate advanced liver disease and/or extensive portosystemic collateral formation (shunting). Two major forms of hepatic encephalopathy are recognized:
Acute hepatic encephalopathy usually occurs in the setting of fulminant hepatic failure. Cerebral edema plays a more important role in this setting: coma is common and mortality is very high .
Chronic hepatic encephalopathy usually occurs with chronic liver disease, commonly manifests as subtle disturbances of neurological function, and is often reversible.
The pathogenesis of hepatic encephalopathy is unknown but is thought to involve the inadequate hepatic removal of predominantly nitrogenous compounds or other toxins ingested or formed in the gastrointestinal tract. Inadequate hepatic removal results from impaired hepatocyte function as well as the extensive shunting of splanchnic blood directly into the systemic circulation via portosystemic collaterals. Nitrogenous and other absorbed compounds are thought to gain access to the central nervous system, leading to disturbances in neuronal function. Ammonia, derived from both amino acid deamination and bacterial hydrolysis of nitrogenous compounds in the gut, has been strongly implicated in the pathogenesis of hepatic encephalopathy. However, blood levels of ammonia correlate poorly with the presence or degree of encephalopathy. Other proposed neurotoxins include gamma-aminobutyric acid, mercaptans, and short chain fatty acids. Mercaptans are also thought to produce the characteristic breath odor (fetor hepaticus) of patients with chronic liver failure. Another hypothesis suggests that an imbalance between plasma branched-chain and aromatic amino acids, a common consequence of severe liver disease, leads to decreased synthesis of normal neurotransmitters and to increased formation of “false neurotransmitters” from aromatic amino acids in the central nervous system.
The clinical features of hepatic encephalopathy include disturbances of higher neurological function (intellectual and personality disorders, dementia, inability to copy simple diagrams [i.e., constructional apraxia], disturbance of consciousness), disturbances of neuromuscular function (asterixis, hyperreflexia, myoclonus), and rarely, a Parkinson-like syndrome and progressive paraplegia. As with other metabolic encephalopathies (which may show many of the signs of hepatic encephalopathy) asymmetrical neurological findings are unusual but can occur, and brain stem reflexes (e.g., pupillary light, oculovestibular, and oculocephalic responses) are preserved until very late. Hepatic encephalopathy is usually divided into stages according to its severity . Subtle disorders of psychomotor function may exist in many patients with cirrhosis in whom conventional neurological examination is normal. Such subclinical encephalopathy (termed stage 0 encephalopathy) is of importance in that it may impair work performance.
The differential diagnosis of hepatic encephalopathy includes hypoglycemia, subdural hematoma, meningitis, and sedative drug overdosage, all of which are common in patients, particularly alcoholics, with liver disease.
- Potassium Homeostasis
- PULMOIIARY FUNCTION EVALUATION
- Procainamide
- CYSTIC FIBROSIS
- ARTERJAL BLOOD GASES
- Aminoaciduria
- CARDIAC TUMORS
- DIAGNOSIS AND EVALUATION
- MEDIASTINAL DISEASE
- Ultrasound and Computed Tomography
- CLASSIFICATION OF THE MALABSORPTION SYNDROMES
- APPROACH TO THE PATIENT WITH SUSPECTED OR CONFIRMED ARRHYTHMIAS
- NONMEDICAL MANAGEMENT OF ANGINA PECTORIS
- TREATMENT
- Bretylium Tosylate
- SPECIFIC ENTITIES - DISEASES WITH KFiOWIi ETIOLOGIES -
- Renal Tubular Acidosis
- Chronic Interstitial Nephritis
- SUDDEN CARDIAC DEATH
- INVASIVE DIAGNOSTIC TECHNIQUES
- NORMAL ABSORPTION
- Disopyramide
- Etiology and Pathogenesis
- OTHER THERAPEUTIC MODALITIES
- THE APPROACH TO THE PATIENT WITH GASTROINTESTINAL HEMORRHAGE
- CONSTRICTIVE PERICARDITIS
- NORMAL ESOPHAGEAL PHYSIOLOGY
- PATHOLOGY
- OBLITERATIVE OR OBSTRUCTIVE PULMONARY HYPERTENSION
- Diagnosis
- DIFFUSE INFILTRATIVE DISEASES OF THE LUNG
- Elimination of Waste Products of Metabolism and Drugs
- Other Clearly Extrinsic Causes of Diffuse Infiltrative Lung Disease
- Metabolism of Drugs in Patients with Renal Insufficiency
- Sodium Retention